Alpha-Keto Acid Dehydrogenase Complexes

Chapter 1 Interaction of protein domains in the assembly and mechanism of 2-oxo acid dehydrogenase multienzyme complexes

Chapter 2 Probing the active site of mammalian pyruvate dehydrogenase

Chapter 3 Role of the E2 core in the dominant mechanisms of regulatory control of mammalian pyruvate dehydrogenase complex

Chapter 4 Lipoamide dehydrogenase

Chapter 5 Plant pyruvate dehydrogenase complexes

Chapter 6 Regulation of the pyruvate dehydrogenase complex during the aerobic/anaerobic transition in the development of the parasitic nematode, Ascaris suum

Chapter 7 Structure, function and assembly of mammalian branched-chain α-ketoacid dehydrogenase complex

Chapter 8 Lipoylation of E2 component

Chapter 9 Pyruvate dehydrogenase phosphatase

Chapter 10 The mitochondrial α-ketoacid dehydrogenase kinases: Molecular cloning, tissue-specific expression and primary structure analysis

Chapter 11 Shorter term and longer term regulation of pyruvate dehydrogenase kinases

Chapter 12 Hormonal and nutritional modulation of PDHC activity status

Chapter 13 Regulation of branched-chain α-keto acid dehydrogenase complex in rat liver and skeletal muscle by exercise and nutrition

Chapter 14 Dephosphorylation of PDH by phosphoprotein phosphatases and its allosteric regulation by inositol glycans

Chapter 15 Long-term regulation and promoter analysis of mammalian pyruvate dehydrogenase complex

Chapter 16 The sperm-specific pyruvate dehydrogenase E1α genes

Chapter 17 Molecular defects of the branched-chain α-keto acid dehydrogenase complex: Maple syrup urine disease due to mutations of the E1α or E1β subunit gene

Chapter 19 Multigenic basis for maple syrup urine disease with emphasis on mutations in branched chain dihydrolipoyl acyltransferase

Chapter 20 Structure and chromosomal localization of the human 2-oxoglutarate dehydrogenase gene

Chapter 21 Pyruvate dehydrogenase complex as an autoantigen in primary biliary cirrhosis