36 th Hemophilia Symposium Hamburg 2005

Table of Contents

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   Book Overview
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   Chapter 1 HIV Infection and Causes of Death in Patients with Hemophilia in Germany (Year 2004/2005 Survey)
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   Chapter 2 Development of the German Hemophilia Register
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   Chapter 3 National Hemophilia Registry - Source of Information about the Quality of Hemophilia Medical Care in a Developing Country
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   Chapter 4 Regulation of Factor VIII Life-Cycle by Receptors from LDL Receptor Superfamily
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   Chapter 5 Update of the Inhibitor-Immunology-Study
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   Chapter 6 Therapy of Acquired Hemophilia - Immunoadsorption and Rituximab Treatment for Immunosuppression and Substitution of Coagulation Factors
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   Chapter 7 Osteoporosis and Hemophilia - Is there a Correlation and Is there a Problem?
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   Chapter 8 Orthopedic Evaluation of the Lower Extremity in 249 Children: A Multicenter Trial
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    Chapter 9 Simultaneous Bilateral Total Knee Arthroplasty in Hemophilic Arthopathy
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    Chapter 10 Alternative Therapy such as the Acupuncture of the Skull for Hemophilic Arthropathy
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    Chapter 11 Endoprosthetics of Large Joints in Patients Infected with HIV
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    Chapter 12 Factor VIII Methods: Which Assay Principle for which Indication?
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    Chapter 13 Global ECAT Survey on Factor VIII Inhibitor Testing: Results of an Inter-Laboratory Pilot Study
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    Chapter 14 A Practical Concept for Pre-Operative Identification and Improved Management of Patients at Risk for Bleeding
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    Chapter 15 Intravascular Tissue Factor in Cord vs Adult Whole Blood
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    Chapter 16 Perioperative Coagulation Screening in Children - Reasons and Results
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    Chapter 17 Thrombin Generation in Children
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    Chapter 18 Working-Group of the German Hemophilia Assistants - History, Purpose and Goals
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    Chapter 19 The Endogenous Thrombin Potential as a New Parameter for the Peri-Operative Monitoring in Conjunction with Endo-Prosthetic Supply due to Hemophilic Arthropathy
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    Chapter 20 Identification of Inhibitor Epitopes in Acquired Hemophilia by Phage Display
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    Chapter 21 Spectrum of Molecular Defects and Mutation Detection Rate in Patients with Mild and Moderate Hemophilia A
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    Chapter 22 Recombinant Factor VIIa for Major Surgery in Severe Factor XI Deficiency: Pharmacodynamic Monitoring Using Thromboelastometry
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    Chapter 23 Establishment of a Web-Based Documentation System for Quality Assurance of Hemophilia Treatment in Mecklenburg/Western Pomeranian: a Pilot Study
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    Chapter 24 Successful Angiographic Embolization of Recurrent Elbow Joint Bleeds in one Patient with Severe Hemophilia A
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    Chapter 25 Evaluation of Thrombotic Events in Hemophiliacs Undergoing Major Orthopedic Surgery Without Thrombosis Prophylaxis
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    Chapter 26 Motivating Patients and Parents to Document Treatment Correctly
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    Chapter 27 Fit for Life Competition: Everyone’s a Winner
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    Chapter 28 Blood Borne Infections in Hemophiliacs in a Developing Country. A Single Center Experience
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    Chapter 29 Hemophilia Center Frankfurt - Twinning Center for Nairobi/Kenya
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    Chapter 30 Economic Evaluation of Orthopedic and Surgical Interventions in Hemophiliacs - Not Only Direct Medical Costs Matter
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    Chapter 31 The Occurrence of Factor VIII Inhibitor in a Patient with Mild Hemophilia A - During Treatment with Interferon for Chronic Hepatitis C
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    Chapter 32 Severe Hemophilia A Patient with High-Titer Inhibitor, use of TGA in the Monitoring of Bypassing Therapy
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    Chapter 33 EUREKA - an European Registry for Orthopedic Surgery in Hemophiliacs with Inhibitors
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    Chapter 34 Double Balloon Enteroscopy (DBE) with Argon Plasma Laser Coagulation (APC) for a Patient with Heyde’s Syndrome
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    Chapter 35 Successful Liver Transplantation in a Patient with Anti-Thrombocyte Antibodies and Severe Hemophilia A
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    Chapter 36 Peri- and Postoperative Course of 95 Patients with von-Willebrand’s Disease
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    Chapter 37 Pregnancy in a Patient with Congenital Antithrombin Deficiency
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    Chapter 38 Successful Inhibitor-Elimination with Rituximab in Acquired Hemophilia A and a Patient with a Carrier Status for Hemophilia A: Two Case Reports
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    Chapter 39 An Interesting Family Case of von-Willebrand-Syndrome
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    Chapter 40 Clinical Manifestations of Dysfibrinogenemia in Relation to the Fibrinogen Gene Mutation
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    Chapter 41 Thrombin Generation in a Hemophilic Newborn
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    Chapter 42 Rapid and Sensitive Detection of Heterozygous Deletions of one or more Exons in Hemophilia A Females by Multiplex PCR and DHPLC Technique
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    Chapter 43 Molecular Genetic Analysis in Patients with Inherited Factor V Deficiency
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    Chapter 44 Expression Analysis of C1-Inhibitor Mutants Confirms Causality of Missense Mutations for Hereditary Angioedema
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    Chapter 45 Expression of the γ-Glutamyl Carboxylase (GGCX) Containing the Arg485Pro Mutation Found in two Unrelated VKCFD1 Patients
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    Chapter 46 Concentration of Soluble Endothelial Protein C Receptor (EPCR) in Plasma in Relation to Age, Sex, BMI and Hemostasis Parameters
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    Chapter 47 Thrombin Generation is Age-Dependent in Children as well as in Adults
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    Chapter 48 Effects of PFA-100 in Preoperative Screening for von Willebrand Disease in 310 Patients
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    Chapter 49 Control of Aspirin Effect in Chronic Cardiovascular Patients Using two Whole Blood Platelet Function Assays: PFA-100 and Multiple Electrode Aggregometry
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    Chapter 50 Difficulties in the Interpretation of the Term »Patient-Related« in the Scope of the Introduction of a Remuneration of Additional Payments According to the OPS
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    Chapter 51 Factor VIII as Positive Regulator of Activated Platelets
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    Chapter 52 Characterization of Three Novel Mutations in the Sodium Binding Site of Coagulation Factor X
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    Chapter 53 Characterization of a Mutation in the 5′ Flanking Region and a Novel IVS7 Splice site Mutation in a Patient with Severe FVII Deficiency
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    Chapter 54 On the Molecular Basis of Warfarin Resistance in Rats
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    Chapter 55 Influence of Factor V HR2 on Endogenous Thrombin Potential and Clinical Phenotype in Factor VII Deficiency
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    Chapter 56 Splice Site Mutations Effect on the <Emphasis Type="Italic">F8</Emphasis> mRNA Splicing
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    Chapter 57 Species-Specific Variation of VKORC1-Activity and Resistance to Warfarin
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    Chapter 58 Various Missense Mutations in the Vitamin K Epoxide Reductase Complex Subunit 1 (VKORC1) Cause Hereditary Coumarin Resistance
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    Chapter 59 Establishment of an International Registry of Patients with Congenital FXIII Deficiency
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    Chapter 60 The Impact of Freezing of Plasma Samples, AB0 Blood Group and Acute-Phase Reaction on Detecting Mild Factor VIII Deficiency and Increased Factor VIII Levels as a Risk Factor for Venous Thromboembolism
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    Chapter 61 Thrombin Generation in Severely Obese Children