Current Views of Fatty Acid Oxidation and Ketogenesis

Table of Contents

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   Book Overview
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   Chapter 1 Biogenesis of the Rat Liver Mitochondrial Carnitine Palmitoyltransferase I
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   Chapter 2 Subcellular Distributuon of Mitochondrial Carnitine Palmitoyltransferase I in Rat Liver
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   Chapter 3 Topology of Hepatic Mitochondrial Carnitine Palmitoyltransferase I
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   Chapter 4 Possible Involvement of Cytoskeletal Components in the Control of Hepatic Carnitine Palmitoyltransferase I Activity
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   Chapter 5 Effects of 3-Thia Fatty Acids on β-Oxidation and Carnitine Palmitoylatransferase I Activity in Cultured Rat Hepatocytes
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   Chapter 6 Carnitine Acyltransferases and Associated Transport Processes in the Endoplasmic Reticulum
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   Chapter 7 Reciprocal Enzymatic Interference of Carnitine Palmitoyltransferase I and Glycerol-3-Phosphate Acyltransferase in Purified Liver Mitochondria
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   Chapter 8 Characterization of a Response Element for Peroxisomal Proliferator Activated Receptor (PPRE) in Human Muscle-type Carnitine Palmitoyltransferase I
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    Chapter 9 Kinetic Investigation of Carnitine Palmitoyltransferases in Homogenates of Human Skeletal Muscle Using L-amino-Carnitine and Malonyl-CoA
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    Chapter 10 Processing of Carnitine Octanoyl Transferase pre-mRNAs by cis and trans -splicing
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    Chapter 11 Selective Modulation of Carnitine Long-chain Acyltransferase Activities
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    Chapter 12 Confocal Laser Scanning Microscopy of Human Skin Fibroblasts Showing Transient Expression of a Green Fluorescent Carnitine Palmitoyltransferase 1 Fusion Protein
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    Chapter 13 Carnitine Biosynthesis
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    Chapter 14 Hypolipidemic 3-Thia Fatty Acids
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    Chapter 15 Molecular Mechanisms of Fatty Acid β -Oxidation Enzyme Catalysis
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    Chapter 16 Control of Mitochondrial β -Oxidation at the Levels of [NAD + ]/[NADH] and CoA Acylation
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    Chapter 17 Production and Export of Acylcarnitine Esters by Neonatal Rat Hepatocytes
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    Chapter 18 Tissue Specific Differences in Intramitochondrial Control of β -Oxidation
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    Chapter 19 Endotoxin-Induced Changes in Very-Low-Density Lipoprotein and Myocardial Utilisation of Triacylglycerol from Abnormal VLDL in the Rat
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    Chapter 20 Effect of Valproic Acid on the Expression of Acyl-CoA Dehydrogenases in Various Tissues
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    Chapter 21 Formation of a Human “Electron Transferring Flavoprotein”
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    Chapter 22 Cloning and Regulation of Peroxisome Proliferator-Induced Acyl-CoA Thioesterases From Mouse Liver
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    Chapter 23 Metabolic Effects of 3-Thia Fatty Acid in Cancer Cells
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    Chapter 24 Poorly Oxidizable Fatty Acid Analogues Inhibit the Proliferation of Cancer Cells in Culture
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    Chapter 25 The Role of PPARα as a“lipostat” Transcription Factor
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    Chapter 26 The Hypolipidaemic Effect of EPA is Potentiated by 2- and 3-Methylation
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    Chapter 27 Is it Time to Reconsider the Role of CPT I in Control of Hepatic Ketogenesis?
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    Chapter 28 Developmental Comparison of Human and Rat Hepatic Mitochondrial 3-Hydroxy-3-Methylglutaryl-CoA Synthase
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    Chapter 29 Regulation of the ketogenic enzyme mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase in astrocytes and meningeal fibroblasts. Implications in normal brain development and seizure neuropathologies.
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    Chapter 30 Studies on Regulation of the Peroxisomal β -Oxidation at the 3-Ketothiolase Step
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    Chapter 31 Role and Organization of Peroxisomal β -Oxidation
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    Chapter 32 Hepatic α -Oxidation of Phytanic Acid
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    Chapter 33 Functions and Dysfunctions of Peroxisomes in Fatty Acid α - and β -Oxidation
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    Chapter 34 Enzymology of β -Oxidation of (Poly)unsaturated Fatty Acids
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    Chapter 35 The Effect of β-Oxidable and Non- β-Oxidable Thia Fatty Acids on Fatty Acid Metabolism
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    Chapter 36 EPA and DHA Possess Different Metabolic Properties
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    Chapter 37 The Use of [9,10- 3 H]Myristate, [9,10- 3 H]Palmitate and [9,10- 3 H]Oleate for the Detection and Diagnosis of Medium and Long-Chain Fatty Acid Oxidation Disorders in Intact Cultured Fibroblasts
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    Chapter 38 Rapid Diagnosis of Organic Acidemias and Fatty-acid Oxidation Defects by Quantitative Electrospray Tandem-MS Acyl-Carnitine Analysis in Plasma
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    Chapter 39 Genetics of Carnitine Palmitoyltransferase II Deficiencies
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    Chapter 40 Identification of a Missense Mutation in a Patient with Lethal Carnitine Acyl-Carnitine Carrier Deficiency
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    Chapter 41 MCAD Deficiency
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    Chapter 42 D-Hydroxyacyl-CoA Dehydrogenase Deficiency
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    Chapter 43 Phytanoyl-CoA Hydroxylase Deficiency
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    Chapter 44 Rationale for a Conditional Knockout Mouse Model to Study Carnitine Palmitoyltransferase I Deficiencies
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    Chapter 45 Biochemical Characterisation of Mutations of Human Medium-Chain Acyl-CoA Dehydrogenase
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    Chapter 46 Lessons Learned from The Mouse Model of Short-Chain Acyl-CoA Dehydrogenase Deficiency